Synonym(s)
angiokeratomas; Angiokeratomas; Haemangiectasia circumscriptum superficialis
DefinitionThis section has been translated automatically.
- Heterogeneous group of congenital (naevi) or acquired hemangiomas or vascular ectasias in which the hyperkeratotic, wart-like surface was originally decisive for the naming. However, hyperkeratosis or the wart-like clinical aspect is often not a leading feature or is missing completely. Therefore, a uniform etiological bracket is missing, which defines the generic term "angiokeratome" for this heterogeneous group of agiomas.
- Most so-called angiokeratomas are histologically capillary or cavernous hemangiomas or mixed images or, as in the case of scrotal or vulval angiokeratomas ( Angiokeratoma scroti et vulvae), phlebectasia.
- The aetiological classification of Mibelli's angiokeratoma, which occurs mainly in adolescents on fingers and toes, is not clear.
- Angiokeratoma corporis diffusum as well as fucosidosis and beta-mannosidosis are dermatological symptoms of lysosomal storage diseases (lack of alpha- or beta-galactosidase; fucosidase, mannosidase).
ClassificationThis section has been translated automatically.
Angiokeratomas include:
- Angiokeratoma Mibelli
- Angiokeratoma scroti et vulvae (Fordyce)
- Angiokeratome, solitary
- angiokeratoma circumscriptum
- Angioeratomas, acral pseudolymphomatous childhood (entity disputed).
Angiokeratomas are observed in the following lysosomal storage diseases and shape the clinical picture dermatologically:
- Angiokeratoma corporis diffusum (Fabry disease - alpha galactosidase deficiency)
- Fucosidosis
- Beta-mannosidosis
- Aspartyl glucosaminuria.
TherapyThis section has been translated automatically.
See under the respective clinical picture.
Outgoing links (10)
Angiokeratoma circumscriptum; Angiokeratomas, acral pseudolymphomatous childhood; Angiokeratome, solitary; Aspartyl glucosaminuria; Beta-mannosidosis; Cutaneous vascular tumors (overview); Fabry's disease; Fucosidosis; Mibelli's angiokeratoma; Scrotal and vulval angiosclerosis;Disclaimer
Please ask your physician for a reliable diagnosis. This website is only meant as a reference.