Canaliculus pili Q84.1

Last updated on: 29.10.2020

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Synonym(s)

Cheveux incoiffables; Glass wool hair; Hair uncombinable; Pili trianguli et canaliculi; Uncombatable hair; Uncombed hair syndrome; Uncombinable hair syndromes; Unstylishable hair

History
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Dupré, 1973

Definition
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Sletene, a hair anomaly characterized by so-called furrowed hair, which is not syndromal, harmless and only cosmetically disturbing. Sporadic and familial occurrence is possible.

Etiopathogenesis
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Probably autosomal dominant with varying degrees of penetrance of inherited ectodermal defect. Sporadic occurrence has also been described.

Manifestation
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Occurs in the 1st year of life, partly already from birth.

Clinical features
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Hair that feels rough, dry, frizzy, hard, protruding disorderly from the scalp and therefore undoable, mostly blonde hair. Brushing and combing are impossible. Eyebrows, eyelashes and body hair are normal. The hair appears shimmering in the light and reminds of Pili torti or Pili pseudoanulati.

Diagnosis
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In light microscopy, the cross-section of the hair shaft is rather triangular or kidney-shaped (normal: round or oval). The hair shaft anomaly is best shown by means of the so-called shrink tube technique.

Therapy
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Not known, greasy care products. Successful therapy attempts with biotin are described in isolated cases. Clinical picture can be improved by greasing or gel applications.

Progression/forecast
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Usually improvement or even normalization of the findings over the years, often after entering puberty.

Literature
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  1. Braun-Falco O et al. (1982) On the syndrome: Uncombinable hair. Dermatologist 3: 366-372
  2. Dupré A, Rochiccioli P, Bonafé JL (1973) "Cheveux incoiffables": anomalie congenitale des cheveux. Bull Soc Franc Dermatol Syph 80: 111-112
  3. Dupre A, Bonafe JL (1978) A new type of pilar dysplasia. The uncompable hair syndrome with pili trianguli et canaliculi. Arch Dermatol Res 261: 217-218
  4. Hicks J, Metry DW, Barrish J, Levy M (2001) Uncombable hair (cheveux incoiffables, pili trianguli et canaliculi) syndrome: brief review and role of scanning electron microscopy in diagnosis. Ultrastruct Pathol 25: 99-103
  5. Ludwig E (1987) Pili canaliculi, a type of uncombed hair. dermatologist 38: 727-732

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Last updated on: 29.10.2020