Angioma serpiginosum L81.7

Author: Prof. Dr. med. Peter Altmeyer

All authors of this article

Last updated on: 29.10.2020

Dieser Artikel auf Deutsch

Synonym(s)

Angiektasia serpiginosum Hutchinson; Angioma serpiginosum Crocker; Angioma serpiginosum Hutchinson; infective angioma Hutchinson

History
This section has been translated automatically.

Hutchinson, 1889; Radcliffe Crocker, 1893

Definition
This section has been translated automatically.

Rare, superficial, nevoidal vascular neoplasms, occurring predominantly in girls (during puberty) and young women (relapses during pregnancy possible).

Occasionally associations with systemic diseases have been described (Sjögren's syndrome, primary biliary cirrhosis, paraproteinemia), without a pathogenetic explanation for these comorbidities.

Occurrence/Epidemiology
This section has been translated automatically.

Gynecotropy: Women are affected about 9 times more often than men.

Etiopathogenesis
This section has been translated automatically.

Unknown.

Manifestation
This section has been translated automatically.

Mostly occurring in childhood (80% of patients are affected before the age of 18). Rarely present at birth.

Localization
This section has been translated automatically.

Thighs, buttocks, mamma, arms, trunk parts near the extremities.

Clinical features
This section has been translated automatically.

Disseminated, 1-2 mm in size, bright red to purple-coloured, sometimes non-removable, dot-shaped spots. Occasionally also telangiectasias. Serpiginous, gyrated or linear patterns are produced by grouped arrangement. Occurring on one or both sides (rather symmetrical). Palms, soles and the mucous membranes close to the skin remain free.

Manifestations along the Blaschko lines are rarely described.

Histology
This section has been translated automatically.

Convolute dilated capillaries with or without thickening of the vessel wall in the papillary stratum, sometimes also capillary proliferation and erythrocyte extravasations. No inflammatory infiltrates.

Differential diagnosis
This section has been translated automatically.

Therapy
This section has been translated automatically.

Laser therapy(e.g. pulsed dye laser) can be applied with good results.

Alternative: diathermy needle sclerotherapy.

Supplementary: cosmetic cover.

Progression/forecast
This section has been translated automatically.

Healing without atrophy possible, usually after years.

Literature
This section has been translated automatically.

  1. Al Hawsawi K et al (2003) Linear angioma serpiginosum. Pediatric dermatol 20: 167-168
  2. Chavaz P, Laugier P (1981) Angioma serpiginosum Hutchinson: ultrastructural study (author's transl). Ann Dermatol Venereol 108: 429-436
  3. The D et al (2016) Blaschko-linear angioma serpiginosum. Indian JDermatol
    Venereol Leprol 82:335-337.

  4. Gerbig A et al (1995) Angioma serpiginosum, a skin change along the Blaschko lines. Dermatologist 46: 847-849

  5. Kalisiak MS et al (2008) Angioma serpiginosum with linear distribution: casereport
    and review of the literature. J Cutan Med Surg 12:180-183.

  6. Katta R et al (2003) Angioma serpiginosum with extensive cutaneous involvement. J Am Acad Dermatol 42: 384-385

  7. Namazi MR et al (2003) Angioma serpiginosum. Dermatol Online J 9: 19
  8. Radcliffe-Crocker H (1893) Diseases of the skin: their description, pathology, diagnosis, and treatment, with special reference to the skin eruptions of children. P. Blakiston, son & Co, Philadelphia, S. 646
  9. Sandhu K, Gupta S (2005) Angioma serpiginosum: report of two unusual cases. J Eur Acad Dermatol Venereol 19: 127-128

Disclaimer

Please ask your physician for a reliable diagnosis. This website is only meant as a reference.

Authors

Last updated on: 29.10.2020