Acroangiodermatitis I87.2

Author: Prof. Dr. med. Peter Altmeyer

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Last updated on: 29.10.2020

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Synonym(s)

Acroangiodermatitis; caposiform acroangiodermatitis; Caposiform acroangiodermatitis; Mali Syndrome; Pseudo-Kaposi's sarcoma (Mali type); Pseudosarcoma Kaposi

History
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Mali, 1965

Definition
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A reactive vascular disease with lobular structures belonging to the group of pseudo-Kaposi sarcomas, which occurs in advanced chronic venous insufficiency.

Etiopathogenesis
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Chronic venous insufficiency; other causes: vascular malformations, trauma, hemodialysis shunts.

Manifestation
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Especially in the 4th-6th decade of life; women are 8-10 times more frequently affected than men.

Localization
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Mainly toes and back of the foot, but also lower legs; usually bilaterally symmetrical.

Clinical features
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Blurred, deep red to reddish brown, usually less symptomatic papules and plaques with smooth or scarlatinous scaly surface, which develop from the smallest red papules (see edge of the lesions). In addition, signs of chronic venous insufficiency, such as a feeling of heaviness in the extremities, oedema, dermatosclerosis and/or ulcer formation.

Histology
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Acanthosis, capillary proliferations and dilatations in the upper corium, erythrocyte extravasations, round cell infiltrates, all in all reminding of an initial Kaposi sarcoma.

Differential diagnosis
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Kaposi's sarcoma, purpura jaune d`ocre, leukocytoclastic vasculitis, Stewart's blood color syndrome.

Therapy
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Literature
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  1. Brenner S, Martinez de Morentin E (2001) What's new in pseudo-Kaposi's sarcoma. J Eur Acad Dermatol Venereol 15: 382-384
  2. Kapdagli H et al (1998) Pseudo-Kaposi's sarcoma (Mali type). Int J Dermatol 37: 223-225
  3. Krengel S et al (1999) Kaposiforms, HHV-8 negative acroangiodermatitis in chronic venous insufficiency. Dermatologist 50: 208-213
  4. Larralde M et al (2001) Pseudo-Kaposi sarcoma with arteriovenous malformation. Pediatric dermatol 18: 325-327
  5. Mali JWH, Kuiper JP, Hamers AA (1965) Acro-Angiodermatitis of the Foot. Arch Dermat 92: 515-518

Disclaimer

Please ask your physician for a reliable diagnosis. This website is only meant as a reference.

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Last updated on: 29.10.2020