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DefinitionThis section has been translated automatically.
Familial hepatocellular disorder of bilirubin metabolism caused by a microsomal (bilirubin conjugation disorder - Crigler-Najjar syndrome type I and type II) or postmicrosomal preterminal disorder (isolated secretion disorder of conjugated bilirubin - Dubin-Johnson syndrome, Rotor syndrome).
ClassificationThis section has been translated automatically.
With elevated unconjugated (indirect) bilirubin
- Crigler-Najjar syndrome type I
- Crigler-Najjar syndrome type II (Arias syndrome)
- Gilbert-Meulengracht syndrome
With elevated conjugated (direct) bilirubin
- Dubin-Johnson syndrome (E 80.6)
- Rotor syndrome (E 80.6)
- Idiopathic recurrent cholestasis (Summerskill-Tygstrup) E83.1
Incoming links (1)
Icterus intermittens juvenilis Meulengracht; Gilbert-Syndrom; Morbus Meulengracht; Gilbert-Meulengracht-Syndrom; ;Outgoing links (5)
Crigler-najjar syndrome; Dubin-johnson syndrome; Icterus intermittens juvenilis Meulengracht; Gilbert-Syndrom; Morbus Meulengracht; Gilbert-Meulengracht-Syndrom; ; Rotor syndrome; Summerskill-tygstrup syndrome;Disclaimer
Please ask your physician for a reliable diagnosis. This website is only meant as a reference.