Lentiginosis partiale unilaterale L81.4

Lentiginosis of the skin whose entity has yet to be secured. It is characterized by numerous grouped, mostly segmentally arranged, strictly unilaterally localized lentigines in otherwise normal skin. There are associations with segmental neurofibromatosis type V(neurofibromatosis, segmental), especially when café-au-lait spots are simultaneously detectable in the affected segment. Further associated symptoms are described:

• Cafe-au-lait stains
• Bulbar pigmentation spots
• Nevus Ota

First manifestation: 1-5 years of age

First manifestation: 1-5 years of age

1. González-Sixto B et al (2009) Partial unilateral lentiginosis associated with nevus of Ota. J Am Acad Dermatol 63:353-355
2. In SI, Kang HY (2008). Partial unilateral lentiginosis colocalized with naevus depigmentosus. Clin Exp Dermatol33:337-339
3. Rao GS (2004) Partial unilateral lentiginosis with Lisch nodules: a forme fruste of segmental neurofibromatosis? Indian J Dermatol Venereol Leprol 70:114-115
4. Toelle SP et al (2006) Association of lentiginous mosaicism and congenital cataract in a girl. Eur J Dermatol 16:360-362