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AcroangiodermatitisI87.2
Synonym(s)
Acroangiodermatitis; caposiform acroangiodermatitis; Caposiform acroangiodermatitis; Mali Syndrome; Pseudo-Kaposi's sarcoma (Mali type); Pseudosarcoma Kaposi
HistoryThis section has been translated automatically.
Mali, 1965
DefinitionThis section has been translated automatically.
A reactive vascular disease belonging to the group of pseudo-caposi-sarcomas with capillary neoplasms in the upper corium, which occurs mainly in advanced chronic venous insufficiency but also in the suction area of negative pressure prostheses.
EtiopathogenesisThis section has been translated automatically.
Chronic venous insufficiency. Other causes: vascular malformations, trauma, hemodialysis shunts, negative pressure prostheses.
ManifestationThis section has been translated automatically.
Especially in the 4th-6th decade of life; women are 8-10 times more frequently affected than men.
LocalizationThis section has been translated automatically.
Mainly toes and back of the foot, but also lower legs; usually bilaterally symmetrical.
Clinical featuresThis section has been translated automatically.
Blurred, deep red to reddish brown, usually less symptomatic papules and plaques with smooth or scarlatinous scaly surface, which develop from the smallest red papules (see edge of the lesions). In addition, signs of chronic venous insufficiency, such as a feeling of heaviness in the extremities, oedema, dermatosclerosis and/or ulcer formation.
HistologyThis section has been translated automatically.
Acanthosis, capillary proliferations and dilatations in the upper corium, erythrocyte extravasations, round cell infiltrates, all in all reminding of an initial Kaposi sarcoma.
Differential diagnosisThis section has been translated automatically.
Kaposi's sarcoma, purpura jaune d`ocre, leukocytoclastic vasculitis, Stewart's blood color syndrome.
TherapyThis section has been translated automatically.
Corresponding to chronic venous insufficiency.
LiteratureThis section has been translated automatically.
- Brenner S, Martinez de Morentin E (2001) What's new in pseudo-Kaposi's sarcoma. J Eur Acad Dermatol Venereol 15: 382-384
- Kapdagli H et al (1998) Pseudo-Kaposi's sarcoma (Mali type). Int J Dermatol 37: 223-225
- Krengel S et al (1999) Kaposiforms, HHV-8 negative acroangiodermatitis in chronic venous insufficiency. Dermatologist 50: 208-213
- Larralde M et al (2001) Pseudo-Kaposi sarcoma with arteriovenous malformation. Pediatric dermatol 18: 325-327
- Mali JWH, Kuiper JP, Hamers AA (1965) Acro-Angiodermatitis of the Foot. Arch Dermat 92: 515-518