Miescher syndrome Q87.27
Synonym(s)
Bloch-Miescher syndrome
History
This section has been translated automatically.
Miescher, 1921
Definition
This section has been translated automatically.
Combination of acanthosis nigricans, mental retardation, hypertrichosis and diabetes mellitus, dental anomalies and cutis verticis gyrata. S.a. o. Cutaneo-ossal syndrome, Cheilitis granulomatosa.
Therapy
This section has been translated automatically.
Cessation of diabetes mellitus. Otherwise symptomatic therapy according to clinic, s.a. hypertrichosis, acanthosis nigricans, cutis verticis gyrata, cheilitis granulomatosa.
Literature
This section has been translated automatically.
- Miescher G (1921) Two cases of congenital familial acanthosis nigricans, combined with diabetes mellitus Dermatol Z (Basel) 32: 276-305
Incoming links (1)
Acanthosis nigricans in hereditary syndromes;Outgoing links (5)
Acanthosis nigricans (overview); Cheilitis granulomatosa; Cutaneous osseous syndrome; Cutis verticis gyrata; Hypertrichoses;Disclaimer
Please ask your physician for a reliable diagnosis. This website is only meant as a reference.