Lymphangioma cavernosum D18.1-

Author: Prof. Dr. med. Peter Altmeyer

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Last updated on: 29.10.2020

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Synonym(s)

cystic lymphangioma; Hygroma cysticum; lymphangioma cysticum

Definition
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The lymphatic malformations affecting the dermatological specialty are mostly subcutaneously or cutaneously-subcutaneously localized lymphatic malformations(lymphangioma), which consist of a bundle of large-volume, cystically expanded lymphatic vascular spaces

The other cavernous lymphatic malformations concern different specialties. They are diagnosed as non-symptomatic (tumor masses) and affect different localizations such as mediastinum, ovaries, kidneys, genitals, etc.

Manifestation
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From birth or in early infancy.

Localization
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Ubiquitous on skin and mucous membranes, especially in the neck, head and extremities.

Clinical features
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Skin-coloured, more rarely bluish (caused by haemorrhaging), cushion-like, succulent, usually blurred, painless tumour of varying size. Depending on the size of the lymphangioma, elephantiasis, macrochelia, macroglossia are possible.

Histology
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  • Differently dilated and calibrated lymph vessels with optically empty lumina. Transitions between thin- and thick-walled, muscularly dilated vessel walls, lymphocytic infiltrate and lymph follicles.
  • Immunohistology: Endothelia pos. for CD31.

Diagnosis
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Differential diagnosis
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Deep-seated infantile hemangioma; lymphangioma-like variant of angiosarcoma; lymphangioma-like Kaposi sarcoma.

Therapy
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Surgical removal if necessary.

Literature
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  1. Bieniasz A et al (1961) A case of lymphangioma cavernosum of the ovary.ginekol Pol 32:667-669.
  2. Chirino-Romo J et al (2014) Unusual diagnosis of an intrathoracic tumor, cavernosum lymphangioma. Case report. Circle 82:537-540.
  3. Khanna S et al (1978) Lymphangioma cavernosum of the ovary. Int Surgery 63:104-105.
  4. Malik NM (1951) Congenital lymphangioma cavernosum. (Report of a case). Indian J Surge 13:82-84.
  5. Rodríguez Reina G et al (1998) Intrascrotal lymphangioma: report of 2 cases and review of the literature. Actas Urol Esp 22:55-59.

Disclaimer

Please ask your physician for a reliable diagnosis. This website is only meant as a reference.

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Last updated on: 29.10.2020