Keratosis palmaris et plantaris cum surditate congenita et leuconychia totalis unguium Q82.8
Synonym(s)
Schwann syndrome
Definition
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Combination of palmoplantar keratoses with leukonychia of all nails and deafness; hyperhidrosis of the hands. Probably irregular dominant inheritance.
Therapy
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Symptomatic.
Incoming links (2)
Keratosis palmoplantaris diffusa with mutations in cathepsin c; Schwann syndrome;Disclaimer
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