Elastorrhexis, papular Q82.8

A rare clinical presentation (fewer than 50 cases have been described in the literature to date) characterized by disseminated, non-follicular, soft, skin-colored, asymptomatic nodules or depressions, each barely the size of a lentil and with a slightly shiny surface.  

Chest, stomach, back.

The entity is controversial; is a "minus" variant of Ehlers-Danlos syndromebeing discussed? 

Reduction or loss of elastic fibres with fragmentation (elastolysis); homogenisation of collagenous connective tissue.

Treatment: There are no known reliable curative treatment options.

1. Flores PB et al. (2010) Papular elastorrhexis: an acquired disorder of elastic tissue. Eur J Dermatol 20:525-526.
2. Panagou E et al. (2019) Pseudoxanthoma elasticum-like papillary dermal elastolysis: a case report and review of the literature. Int J Dermatol 58:93–97.
3. Sears et al. (1988) Papular elastorrhexis: A variant of connective tissue nevus. J Am Acad Dermatol 19:409
4. Sezer E et al. (2018) Papular elastorrhexis: clinical perspectives. Clin Cosmet Investig Dermatol 11:541–544.
5. Xue R et al. (2015) Papular elastorrhexis. Indian J Dermatol Venereol Leprol 81:529–531.
6. Sears et al. (1988) Papular elastorrhexis: A variant of connective tissue nevus. J Am Acad Dermatol 19: 409