Calcinosis dystrophica L94.21

Aetiologically unexplained deposition of calcium salts in pathologically altered cutis, subcutis or muscles, without detectable calcium or phosphate metabolic disturbance.

The term calcinosis dystrophica is generally equated with the terms calcinosis metabolica and calcinosis idiopathica. Dystrophic calcinosis occurs in scars, chronic inflammatory infiltrates, cysts, epitheliomas, carcinomas, hemangiomas in organized thrombophlebitis (phlebolite) and others.

Within dystrophic calcinosis a distinction is made between:

• Calcinosis dystrophica localized
• and
• Calcinosis dystrophica disseminated (previously: Calcinosis metabolica universalis).

Disseminated dystrophic calcinosis is mainly observed in the following systemic diseases:

• Thibièrge-Weissenbach syndrome
• CREST syndrome
• Ehlers-Danlos Syndrome
• Pseudoxanthoma elasticum
• Progeria adultorum