Lymphedema, type meige Q82.0

Author: Prof. Dr. med. Peter Altmeyer

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Last updated on: 29.10.2020

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Synonym(s)

late-onset; lymphedema; Lymphedema; lymphedema late-onset; lymphedema praecox familial; Maladie de Meige; Meige's disease; Meige\'s disease; Meige syndrome; Trophodema; Trophodema type Meige; Type Meige

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History This section has been translated automatically.

Meige, 1889

Definition This section has been translated automatically.

Genetically determined primary lymphedema corresponding to lymphedema, type Nonne-Milroy with further associated symptoms and later manifestation

Etiopathogenesis This section has been translated automatically.

Unknown.

Manifestation This section has been translated automatically.

Puberty. Women are affected twice as often as men.

Clinic This section has been translated automatically.

  • According to the lymphedema, type Nonne-Milroy, s. there.
  • In addition: short stature, mental retardation, hypogenitalism, ptosis of the eyelids, recurrent intrahepatic cholestasis, obesity in the area of the breeches; rarely additional infestation of the genitals, upper extremities, face, larynx and pleura (effusions).
  • Congenital anomalies: partial membranous syndactylia of the toes, distichiasis (double row of eyelashes); myopia; ptosis; yellow nails; extradural cysts and/or vertebral anomalies; cerebrovascular malformations; sensoneural hearing loss; cleft palate. Bronchiectasis.

Therapy This section has been translated automatically.

S.u. lymphedema, nun-milroy type.

Literature This section has been translated automatically.

  1. Figueroa AA, Pruzansky S, Rollnick BR (1983) Meige disease (familial lymphedema praecox) and cleft palate: report of a family and review of the literature. Cleft palate J 20: 151-157
  2. Meige H (1898) Dystrophy oedematose hereditaire. La presse médicale (Paris) 6: 341-343
  3. Meige H (1889) Le trophoedème chronique héréditaire. Nouv iconogr Salpêtrière, Paris, 12: 453-480
  4. Ho WL et al (2003) Radiological features of late-onset lymphoedema in Noonan's syndrome. Pediatric radiol 33: 200-202
  5. Samlaska CP (2002) Congenital lymphedema and distichiasis. Pediatric Dermatol 19: 139-141
  6. Tammer ME et al (2002) Surgical therapy of scrotal edema in elephantiasis congenita hereditaria (Meige type). Urologist A 41: 493-495
  7. Wheeler ES et al (1981) Familial lymphedema praecox: Meige's disease. Plast Reconst Surgery 67: 362-364

Authors

Last updated on: 29.10.2020

Author: Prof. Dr. med. Peter Altmeyer