Bonnet-dechaume-blanc syndromeQ85.8

Author:Prof. Dr. med. Peter Altmeyer

All authors of this article

Last updated on: 29.10.2020

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Synonym(s)

Neuro-Retino Angiomatosis Syndrome; Wyburn-Mason Syndrome

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HistoryThis section has been translated automatically.

Bonnet, Dechaume and Blanc, 1937; Wyburn-Mason, 1943

DefinitionThis section has been translated automatically.

Very rare congenital angiodysplasia syndrome: Combination of a naevus flammeus lateralis in the facial region (inconstant) with malformations of the retinal vessels (aneurysms, tendral angiomas) and the midbrain and brainstem vessels (neurological symptoms).

TherapyThis section has been translated automatically.

Treatment of the skin symptoms, if necessary with laser therapy. Cooperation with neurologists, if necessary ophthalmologists.

LiteratureThis section has been translated automatically.

  1. Bonnet P, Dechaume J, Blanc E (1937) L'anévrysme cirsoïde de la rétine (anévrysme recémeux): ses relations avec l'anéurysme cirsoïde de la face et avec l'anévrysme cirsoïde du cerveau. J Med Lyon 18: 165-178
  2. Wyburn-Mason R (1943) Arteriovenous malformation of the mid-brain and retina, facial naevi, and mental changes. Brain 66: 163-203

Authors

Last updated on: 29.10.2020

Author: Prof. Dr. med. Peter Altmeyer