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Angioma serpiginosumL81.7

Author:Prof. Dr. med. Peter Altmeyer

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Last updated on: 29.10.2020

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Synonym(s)

Angiektasia serpiginosum Hutchinson; Angioma serpiginosum Crocker; Angioma serpiginosum Hutchinson; infective angioma Hutchinson

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HistoryThis section has been translated automatically.

Hutchinson, 1889; Radcliffe Crocker, 1893

DefinitionThis section has been translated automatically.

Rare, superficial, nevoid vascular neoplasms, occurring predominantly in girls and young women. Occasionally associations with systemic diseases have been described (Sjögren's syndrome, primary biliary cirrhosis, paraproteinemia), without a pathogenetic explanation for this association.

EtiopathogenesisThis section has been translated automatically.

Unknown, probably X-linked dominant inherited mosaic.

ManifestationThis section has been translated automatically.

Mostly occurring in childhood (80% of patients are affected before the age of 18). Rarely present at birth. Gynecotropy: Women are affected about 9 times as often as men.

LocalizationThis section has been translated automatically.

Thighs, buttocks, mamma, arms, trunk parts near the extremities.

Clinical featuresThis section has been translated automatically.

Disseminated, 1-2 mm in size, bright red to purple-coloured, sometimes non-removable, dot-shaped spots. Occasionally also telangiectasias. Serpiginous, gyrated or linear patterns are produced by grouped arrangement. Occurring on one or both sides (rather symmetrical). Palms, soles and the mucous membranes close to the skin remain free.

Manifestation along the Blaschko lines is described but rather the rarity.

HistologyThis section has been translated automatically.

Convolute dilated capillaries with or without thickening of the vessel wall in the papillary stratum, sometimes also capillary proliferation and erythrocyte extravasations. No inflammatory infiltrates.

Differential diagnosisThis section has been translated automatically.

Spider veins; Purpura pigmentosa progressiva; Angiokeratoma corporis diffusum; Teleangiectasia hereditaria haemorrhagica.

TherapyThis section has been translated automatically.

Laser therapy(e.g. pulsed dye laser), if necessary diathermy needle sclerotherapy, cosmetic covering.

Progression/forecastThis section has been translated automatically.

Healing without atrophy possible, usually after years.

LiteratureThis section has been translated automatically.

  1. Al Hawsawi K et al (2003) Linear angioma serpiginosum. Pediatric dermatol 20: 167-168
  2. Chavaz P, Laugier P (1981) Angioma serpiginosum Hutchinson: ultrastructural study (author's transl). Ann Dermatol Venereol 108: 429-436
  3. Gerbig A et al (1995) Angioma serpiginosum, a skin change along the Blaschko lines. dermatologist 46: 847-849
  4. Katta R et al (2003) Angioma serpiginosum with extensive cutaneous involvement. J Am Acad Dermatol 42: 384-385
  5. Namazi MR et al (2003) Angioma serpiginosum. Dermatol Online J 9: 19
  6. Radcliffe-Crocker H (1893) Diseases of the skin: their description, pathology, diagnosis, and treatment, with special reference to the skin eruptions of children. P. Blakiston, son & Co, Philadelphia, S. 646
  7. Sandhu K, Gupta S (2005) Angioma serpiginosum: report of two unusual cases. J Eur Acad Dermatol Venereol 19: 127-128

Authors

Last updated on: 29.10.2020

Author: Prof. Dr. med. Peter Altmeyer