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Angiofibroma (overview)D23.0
Synonym(s)
angiofibroma of the mucous membrane; cutaneous angiofibroma
DefinitionThis section has been translated automatically.
A group of benign tumours (hamartomas) on the skin and/or mucous membranes close to the skin that are neither clinically nor histologically detectable as a clear entity. In addition to connective tissue proliferation, the tumours show a prominent vascular richness. Angiofibromas are usually a random histological finding.
Angiofibromas as hamarous malformations:
- In the context of Bourneville-Pringle-phacomatosis, angiofibromas occur systematically (face, periungual fibromas) (the term Adenoma sebaceum for the acne-like angiofibromas of this genodermatosis is a misnomer).
- Tumour-associated genodermatoses include the angiofibromas and connective tissue nevi in MEN-I syndrome and Cowden syndrome.
ClassificationThis section has been translated automatically.
A distinction is made between:
- Angiofibroma (Adenoma sebaceum)
- Angiofibroma, cell-rich
- Nasal papule, fibrous
- Fibroma, periunguales (Koenen tumor)
- Fibrokeratome, acquired, digital
- Wermer syndrome (multiple endocrine neoplasia type 1)
- Cowden's syndrome.
Clinical featuresThis section has been translated automatically.
See below the respective clinical pictures.
TherapyThis section has been translated automatically.
In case of systematized or multiple occurrence, removal by dermabrasion or laser ( CO2 laser). Individual lesions can be removed surgically, e.g. by punch biopsy.
Note(s)This section has been translated automatically.
The previously described "angiofibromas" are to be separated from the rare cell-rich angiofibroma, which occurs mainly as a tumour of the female (or more rarely male) genitals (especially the vulva).