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Angiofibroma (overview)D23.0
Synonym(s)
angiofibroma of the mucous membrane; cutaneous angiofibroma
DefinitionThis section has been translated automatically.
A group of benign tumours (hamartomas) on the skin and/or mucous membranes close to the skin that are neither clinically nor histologically detectable as a clear entity. In addition to connective tissue proliferation, the tumours show a prominent vascular richness. Angiofibromas are usually a random histological finding.
Angiofibromas as hamarous malformations:
- In the context of Bourneville-Pringle-phacomatosis, angiofibromas occur systematically (face, periungual fibromas) (the term Adenoma sebaceum for the acne-like angiofibromas of this genodermatosis is a misnomer).
- Tumour-associated genodermatoses include the angiofibromas and connective tissue nevi in MEN-I syndrome and Cowden syndrome.
ClassificationThis section has been translated automatically.
A distinction is made between:
- Angiofibroma (Adenoma sebaceum)
- Angiofibroma, cell-rich
- Nasal papule, fibrous
- Fibroma, periunguales (Koenen tumor)
- Fibrokeratome, acquired, digital
- Wermer syndrome (multiple endocrine neoplasia type 1)
- Cowden's syndrome.
ClinicThis section has been translated automatically.
See below the respective clinical pictures.
TherapyThis section has been translated automatically.
In case of systematized or multiple occurrence, removal by dermabrasion or laser ( CO2 laser). Individual lesions can be removed surgically, e.g. by punch biopsy.
Note(s)This section has been translated automatically.
The previously described "angiofibromas" are to be separated from the rare cell-rich angiofibroma, which occurs mainly as a tumour of the female (or more rarely male) genitals (especially the vulva).