Agammaglobulinemia acquiredD80.1, D83.0, D83.2 D83.8 D83.9

Author:Prof. Dr. med. Peter Altmeyer

All authors of this article

Last updated on: 29.10.2020

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Synonym(s)

acquired agammaglobulinemia; Immune deficiency syndrome Acquired immune deficiency syndrome; Immunodeficiency

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DefinitionThis section has been translated automatically.

Family history of antibody deficiency syndrome in young girls and older women with a reduction in IgA, IgG and IgM.

Clinical featuresThis section has been translated automatically.

S.u. immune deficiency syndrome variable

DiagnosisThis section has been translated automatically.

IgA, IgG and IgM in the serum is reduced.

TherapyThis section has been translated automatically.

Gamma-globulin substitution (e.g. Intratect) 0.1-0.8 g/kg bw/day every 3-4 weeks, initially start with double the dose (IgG level in plasma should be at least 2 g/l), if necessary prophylactically antibiotics.

Note(s)This section has been translated automatically.

The clinical picture described here is probably identical with the variable immunodeficiency syndrome.

LiteratureThis section has been translated automatically.

  1. Al-Herz W et al (2003) Antibody response in common variable immunodeficiency. Ann Allergy Asthma Immunol 90: 244-247
  2. Barton JC et al (2003) Common variable immunodeficiency and IgG subclass deficiency in central Alabama hemochromatosis probands homozygous for HFE C282Y. Blood Cells Mol Dis 31: 102-111
  3. Sewell WA et al (2003) Therapeutic strategies in common variable immunodeficiency. Drugs 63: 1359-1371
  4. Sidwell RU et al (2002) A case of common variable immunodeficiency presenting with furunculosis. Br J Dermatol 147: 364-367

Authors

Last updated on: 29.10.2020

Author: Prof. Dr. med. Peter Altmeyer