Acrogerie gottronE34.8

Author:Prof. Dr. med. Peter Altmeyer

All authors of this article

Last updated on: 29.10.2020

Dieser Artikel auf Deutsch

Synonym(s)

Acrogerie Gottron family; Family Acrogerie Gottron; Gottron syndrome I; OMIM 201200

Requires free registration (medical professionals only)

Please login to access all articles, images, and functions.

Our content is available exclusively to medical professionals. If you have already registered, please login. If you haven't, you can register for free (medical professionals only).


Requires free registration (medical professionals only)

Please complete your registration to access all articles and images.

To gain access, you must complete your registration. You either haven't confirmed your e-mail address or we still need proof that you are a member of the medical profession.

Finish your registration now

HistoryThis section has been translated automatically.

Gottron, 1941

DefinitionThis section has been translated automatically.

Probably autosomal recessive or autosomal dominant inherited atrophy of skin and subcutaneous fat tissue.

ManifestationThis section has been translated automatically.

From birth or in the first weeks of life, gynaecotropia with a ratio of 3:1.

LocalizationThis section has been translated automatically.

Face and acra.

Clinical featuresThis section has been translated automatically.

Atrophic facial skin, often facial erythema, regional fat loss, frequent scarlatiniform exanthema, micrognathia, acromicity, possibly infantile skeleton of the distal extremities. Combination with systemic scleroderma possible.

Differential diagnosisThis section has been translated automatically.

Progeria infantilis, aplasia cutis congenita, Ehlers-Danlos syndrome, dento-facial syndrome.

TherapyThis section has been translated automatically.

Not known.

LiteratureThis section has been translated automatically.

  1. Blaszczyk M et al (2000) Acrogeria of the Gottron type in a mother and son. Eur J Dermatol 10: 36-40
  2. Butenandt O, Christophers E (1970) The Acrogerie (Gottron). German med Vshr 95: 175-178
  3. Gottron H (1941) Family Acrogeria. Arch Derm 181: 571-583

Authors

Last updated on: 29.10.2020

Author: Prof. Dr. med. Peter Altmeyer