Olfield diseaseQ87.8

Autosomal dominant inherited combination of colon polyposis and multiple atheroma. The atheromas may be present at birth or develop in early childhood. Intestinal polyps usually manifest themselves in the 2nd to 3rd decade of life and contain a high degenerative potential. Probably variant of Gardner syndrome.

Regular monitoring of intestinal polyposis with regard to malignancy criteria (bleeding, obstruction) and treatment by gastroenterologists if necessary. Excision of the atheromas.