Images (2)

Bamboo hairQ80.8

Author:Prof. Dr. med. Peter Altmeyer

All authors of this article

Last updated on: 29.10.2020

Dieser Artikel auf Deutsch

Synonym(s)

Bamboo hair; Bamboo Hair; bamboo hairs (e); invaginated trichorrhexis; OMIM 256500; Trichorrhexis Syndrome

Requires free registration (medical professionals only)

Please login to access all articles, images, and functions.

Our content is available exclusively to medical professionals. If you have already registered, please login. If you haven't, you can register for free (medical professionals only).


Requires free registration (medical professionals only)

Please complete your registration to access all articles and images.

To gain access, you must complete your registration. You either haven't confirmed your e-mail address or we still need proof that you are a member of the medical profession.

Finish your registration now

DefinitionThis section has been translated automatically.

Characteristic hair shaft anomaly (keratinization defect) with microscopically detectable ball-joint like intussusception and distension of the hair shaft. Partial aspect of Netherton syndrome.

EtiopathogenesisThis section has been translated automatically.

The cause of the hair shaft alteration is a cornification disorder, which leads to increased growth of the cells of the outer root sheath; as a result, the cells of the inner root sheath are pressed inwards and enclosed by the outer layers.

ManifestationThis section has been translated automatically.

In newborns in the first weeks of life, usually until the 6th month of life. Girls are more frequently affected.

Clinical featuresThis section has been translated automatically.

Sparse, thin, brittle, dry hair, usually not longer than 3-4 cm.

LaboratoryThis section has been translated automatically.

Increased excretion of arginic succinic acid in urine.

HistologyThis section has been translated automatically.

Nodular distension of the hair shaft due to telescopic compression and invagination.

TherapyThis section has been translated automatically.

No effective therapy known. With increasing age, improvements in hair shaft changes can be detectable.

Progression/forecastThis section has been translated automatically.

Mostly improvement of the hair condition with increasing age.

LiteratureThis section has been translated automatically.

  1. Blaschke S et al (1998) Comel-Netherton syndrome. dermatologist 49: 499-504
  2. Camacho - Martinez F (1989) Localized trichorrhexis nodosa. J Am Acad Dermatol 20: 696-697
  3. Krasagakis K et al (2003) Early development of multiple epithelial neoplasms in Netherton syndrome. Dermatology 207: 182-184
  4. Netherton EW (1958) A unique case of trichorrhexis nodosa - "bamboo hairs Arch Dermatol 78: 483-487
  5. Rudnicka L et al (2018) Trichoscopy in Hair Shaft Disorders. Dermatol Clin 36:421-430.
  6. Steranovic DV et al (1992) Pathogenesis in trichorrhexis invaginata (Bamboo hairs). Eur J Dermatol 2: 15-20
  7. Touraine A, Solente D (1937) Erythrokeratoderma du cuir chevelu et "Trichorrhexis nodosa" familiales. Bull Soc francaise Dermatol Syphiligr 44: 44

Authors

Last updated on: 29.10.2020

Author: Prof. Dr. med. Peter Altmeyer