Unilateral naevoid telangiectasia syndrome I78.8

Author: Prof. Dr. med. Peter Altmeyer

All authors of this article

Last updated on: 29.10.2020

Dieser Artikel auf Deutsch

Synonym(s)

acquired nevoid telangiectasia; Nevoidal telangiectasia syndrome; Spider naevi unilateral; Teleangiectasia naevoide unilateral; Teleangiectasia unilateral; unilateral dermatomal superficial teleangiectasia; Unilateral naevoid telangiectasias; unilateral nevoidal telangiectasia; Unilateral nevoid telangiectasia syndrome; unilateral nevoid teleangiectasia; unilateral Spider Naevi; unilateral telangiectasia; UNTS

Definition
This section has been translated automatically.

Extensive, unilateral, either congenital or acquired districts with dense telangiectasias.

Etiopathogenesis
This section has been translated automatically.

Unknown, often estrogen-induced manifestation. A genetically fixed, increased number of oestrogen or progesterone receptors in the affected vessels is being discussed.

Manifestation
This section has been translated automatically.

Occurs mainly during pregnancy, puberty and alcohol-related liver diseases. Rarely present congenitally.

Localization
This section has been translated automatically.

Preferably face, neck, shoulder-arm region, but also lower extremity and trunk. The arrangement of the lesions largely follows the dermatomes (trigeminal region,C3,C4, thoracic dermatomes, etc.)

Clinical features
This section has been translated automatically.

Discrete or pronounced, usually sharply defined erythema, composed of fine and finest, often star-shaped branched telangiectasias, which largely disappear under glass spatula pressure. No involvement of internal organs or the CNS. No endocrinopathies in congenital forms. Quadrant and half-side formations as well as appearances along the Blaschko lines are possible.

Histology
This section has been translated automatically.

Dermal vasculature.

Therapy
This section has been translated automatically.

Laser treatment with argon or pulsed dye laser leads to improvement of clinical symptoms.

Progression/forecast
This section has been translated automatically.

The intensity of the skin changes usually decreases after the hormonal changes. Nodular transformation as in the naevus flammeus is not likely.

Literature
This section has been translated automatically.

  1. Abeck D et el. (1992) Unilateral naevoidal telangiectasia syndrome case observation and literature review. Z Hautkr 67: 688-690
  2. Raff M et al (1982) Unilateral nevoidal telangiectasia syndrome. Dermatologist 33: 148-151
  3. Sardana K et al (2001) Unilateral nevoid telangiectasia syndrome. J Dermatol 28: 453-454
  4. Uhlin SR et al (1983) Unilateral nevoid telangiectatic syndrome. The role of estrogen and progesterone
    receptors. Arch Dermatol 119:226-228.
  5. Wilkin JK et al (1983) Unilateral dermatomal superficial teleangiectasia. J Am Acad Dermatol 8: 468-477
  6. Wollina U et al (2001) Acquired nevoid telangiectasia. Dermatology 203: 24-26

Disclaimer

Please ask your physician for a reliable diagnosis. This website is only meant as a reference.

Authors

Last updated on: 29.10.2020