Familial anhidrosis L74.84

Last updated on: 29.10.2020

Dieser Artikel auf Deutsch


Anhidrosis Syndrome; Familial anhidrosis; general acquired sudomotor denervation; progressive selective anhidrosis; Ross's syndrome; Ross Syndrome

This section has been translated automatically.

Ross, 1958

This section has been translated automatically.

Disease with a typical symptom triad of tonic pupillary disturbances, loss of autonomic and extraneous reflexes, and bi- or unilateral progressive segmental anhidrosis, which reflexively leads to hyperhidrosis in unaffected segments and to heat intolerance.

This section has been translated automatically.

Unknown, a polytopic disseminated neuropathy in the autonomic nervous system is assumed. Association with autonomic dysfunction is possible.

This section has been translated automatically.

Sweat secretion tests (thermoregulatory, cholinergic, emotional, gustatory irritation and during physical exertion) show a lack of reactive hydrosis.

This section has been translated automatically.

Unchanged number and morphology of sweat glands.

Differential diagnosis
This section has been translated automatically.

Ectodermal dysplasia with hypoanidrosis; Pancoast tumor; hypoanidrosis after sympathectomy, in diabetes mellitus, anemia, intoxications, brain or kidney diseases. Differentiation from Adie syndrome is difficult.

This section has been translated automatically.

By ophthalmologists and neurologists. Avoid extreme temperatures and exsiccative measures such as long and hot showers, hot baths, etc. Bland care with moisturising external agents such as Ungt. emulsif. aq., if necessary with urea additive.

Hyperhidrotic body areas can often be successfully treated with tap water iontophoresis (direct current, 15 Volt, 25 mA) (for exact procedure see there). The commercially available plastic tubs (with electrode connection) are usually designed for hands and feet and must be handmade to fit the affected body area if necessary.

Alternatively, intradermal botulinum injections can be used, which are distributed fan-shaped under hyperhidrotic areas.

This section has been translated automatically.

  1. Chakravarty A et al (2003) Ross syndrome--a case documentation. Acta Neurol Scand 107: 72-73
  2. Itin P et al (1992) The Ross syndrome. Dermatologist 43: 359-360
  3. Reinauer S et al. (1992) Ross syndrome: redefinition and therapy of associated hyperhidrosis by a modified iontophoresis technique. Z Hautkr 67: 615-621
  4. Ross AT (1958) Progressive selective sudomotor denervation. A case with coexisting Adie's syndrome. Neurology 8: 809-817
  5. Weller M, Wilhelm H, Sommer N et al (1992) Tonic pupil, areflexia, and segmental anhidrosis: two additional cases of Ross syndrome and review of the literature. J Neurol 239: 231-234
  6. Yasar S et a. (2010) Ross syndrome: Unilateral hyperhidrosis, adie-pupils and diffuse areflexia. JDDG 12: 1004-1006


Please ask your physician for a reliable diagnosis. This website is only meant as a reference.

Add section

Last updated on: 29.10.2020